E-ISSN 2149-2530
Case report
A Rare Cause of Recurrent Spontaneous Pneumothorax: Birt-Hogg-Dube Syndrome
1 Department of Radiology, Pamukkale University School of Medicine, Denizli, Turkey  
Turk Thorac J ; 5: -
DOI: 10.5152/TurkThoracJ.2018.17045
Key Words: Birt-Hogg-Dube syndrome, cystic lung disease, pneumothorax, pituitary adenoma
Abstract

Birt-Hogg-Dube (BHD) syndrome is an unusual disorder characterized by the triad of cutaneous lesions, renal tumors and lung cysts. In cases with BHD syndrome, the frequency of recurrent pneumothorax is increased due to presence of multiple lung cysts. It is important to evaluate the BHD syndrome in differential diagnosis of recurrent pneumothorax especially with multiple lung cysts predominating in the lung base. In these patients, the presence of accompanying kidney and other tumors should be investigated. Herein, we report a case of BHD syndrome presenting with recurrent pneumothorax.

 

Cite this article as: Karaman E, Ufuk F, Demirci M, Yavaş HG. A Rare Cause of Recurrent Spontaneous Pneumothorax: Birt-Hogg-Dube Syndrome. Turk Thorac J 2018. DOI: 10.5152/TurkThoracJ.2018.17045

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