Abstract

Scimitar syndrome is a natal cardiopulmonary anomaly syndrome that is rarely seen. Partial pulmonary venous return anomaly (PPVRA) comprises 0.5-1% of the congenital cardiac diseases. It may be only a vascular defect but sometimes it can occur together with other congenital cardiac anomalies such as atrial septal defect (ASD). Rarely, PPVRA (3-5%) is present with right pulmonary hypoplasia and dextrocardia, and this is termed Scimitar Syndrome. A forty-two year-old woman suffering from chilling, anorexia, dysphagia, and recurrent pulmonary infection was admitted to our clinic. On physical examination, pectus excavatus was detected by inspection and dextrocardia was suspected by auscultation. These findings were confirmed with postero antero chest X-ray. For the diagnosis, multi slice pulmonary angiography was carried out. A case of Scimitar Syndrome which presented with recurrent pulmonary infection and pulmonary venous return anomaly was reported with a review of literature.