Turkish Thoracic Journal
Poster Presentation

An Unusual Case of Diffuse Pulmonary Meningotheliomatosis Accompanying with Cystic Lung Disease

1.

Clinic of Pulmonology, University of Health Sciences, Dr Suat Seren Chest Diseases and Thoracic Surgery Training and Research Hospital, İzmir, Turkey

2.

Clinic of Pathology, University of Health Sciences, Dr Suat Seren Chest Diseases and Thoracic Surgery Training and Research Hospital, İzmir, Turkey

3.

Clinic of Radiology, University of Health Sciences Dr Suat Seren Chest Diseases and Thoracic Surgery Training and Research Hospital, İzmir, Turkey

4.

Clinic of Thoracic Surgery, University of Health Sciences, Dr Suat Seren Chest Diseases and Thoracic Surgery Training and Research Hospital, İzmir, Turkey

Turk Thorac J 2019; 20: Supplement 326-326
DOI: 10.5152/TurkThoracJ.2019.326
Read: 328 Downloads: 135 Published: 09 August 2019

Introduction: Diffuse pulmonary meningotheliomatosis is a rare disease, presenting with diffuse bilateral pulmonary nodules on HRCT with unclear clinical significance.
 

Case Presentation: A 63-years-old male patient was admitted to our hospital with cough and mild exertional dyspnea. Thorax HRCT scan revealed bilaterally multiple, uniform, thin-walled cysts ranging between 0.5 and 2.5 cm in diameter, diffusely distributing from apex to basis of the lung suggesting lymphangioleiomyomatosis radiologically. Hence the patient was male and symptomatic; further evaluation was needed. Bronchoscopy was nondiagnostic which led to a diagnostic surgical procedure. The patient underwent diagnostic right lower lobe and middle lobe wedge resections. Histopathological examination revealed diffuse meningotheliomatosis unexpectedly. When HRCT findings were reviewed, micronodules smaller than 1 mm were identified. Although the patient only received symptomatic treatment, there were no changes in thorax CT findings through the three years follow up.
 

Conclusion: To our knowledge this case is the first in the literature, demonstrating diffuse meningotheliomatosis accompanied with cystic disease of the lung.

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EISSN 2149-2530