Thoracic Research and Practice
Case report

Kartagener’s Syndrome: A Report of Two Cases

1.

Haseki Eğitim ve Araştırma Hastanesi 4. İç Hastalıkları Kliniği, İstanbul

2.

İstanbul Üniversitesi Cerrahpaşa Tıp Fakültesi Göğüs Hastalıkları Anabilim Dalı, İstanbul

3.

İstanbul Üniversitesi Cerrahpaşa Tıp Fakültesi Histoloji ve Embriyoloji Anabilim Dalı, İstanbul

Thorac Res Pract 2005; 6: Toraks Dergisi 276-279
Read: 1107 Downloads: 533 Published: 18 July 2019

Abstract

Kartagener’s syndrome is a rare autosomal recessive disorder which presents with situs inversus, sinusitis, chronic upper and lower respiratory tract infections during the early phase and bronchiectasis during the late phase of the disease. Excessive sputum production and retension are seen due to impaired cilial activity. Medical treatment is only symptomatic. Clinical and radiological features of the two cases as well as the ultrastructural characteristics of one of them, are presented here. Though cases with Kartagener’s syndrome are frequently discussed in literature, we underdiagnose it in our clinical practice; so we reviewed the available literature at the same time with our cases.

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EISSN 2979-9139