Thoracic Research and Practice
Case report

Primary Alveolar Proteinosis and Review of the Literature

1.

Cumhuriyet University, School of Medicine, Chest Department, Sivas, Turkey

2.

Cumhuriyet University, School of Medicine, Pathology Department, Sivas, Turkey

3.

Cumhuriyet University, School of Medicine, Thoracic Surgery Department, Sivas, Turkey

Thorac Res Pract 2001; 2: Turkish Respiratory Journal 36-39
Read: 420 Downloads: 258 Published: 07 October 2021

Pulmonary alveolar proteinosis is a rare lung disease characterized by the accumulation of lipoproteinaceous material within the alveoli. Analysis of the lipoproteinaceous materials accumulating in the airspaces demonstrates that they represent an abnormal deposition of the normal constituents of surfactant. This deposi­tion is due to an increased secretion or a decreased clearance from the alveoli. We present the diagnosis of primary pulmonary alve­olar proteinosis of a 26 year old female. She was admitted to our department with a dry cough and dyspnea with a slowly progres­sive course. The patient, who was started antituberculous therapy one year ago, had persistent symmetrical airspace consolidation in the chest x-ray. The diagnosis was made by open lung biopsy. Out­patient showed radiological and clinical remission during the time she was hospitalized.

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